Dental implications of tooth-nail dysplasia (Witkop syndrome): a report of an affected family and an approach to dental management.
G.M.Wicomb / L.X.G. Stephen / P. Beighton

Tooth-Nail dysplasia is a rare genetic disorder, which is classified as an ectodermal dysplasia. Diagnostic differentiation from other conditions in this category is necessary for effective dental management and genetic counseling. The oro-dental and clinical manifestations of Tooth-Nail dysplasia in an affected male infant and his father are documented. Other family members have the condition and pedigree data are in keeping with autosomal dominant inheritance.A comprehensive approach to the dental management of an affected child is proposed.