Axenfeld-Rieger Syndrome: Report on dental and craniofacial findings
Dr. Ashok Kumar Jena* / Dr. Om P Kharbanda MDS,M Orth RCS(Edin), FICD,MNAMS**

Axenfeld-Rieger syndrome is a rare autosomal dominant disorder characterized by various ocular and extraocular malformations. Dental abnormalities are considered as definitive features for the diagnosis and differentiation of Rieger syndrome from other anterior chamber of the eye malformations. A case of Rieger syndrome with distinct dental and craniofacial anomalies is described. Significant cranio-dento-facial findings that have been observed are, teeth with short and dilacerated roots, hyperplastic frenums and underdeveloped maxilla. There was an anterior crossbite, bilateral posterior openbite and moderate to severe anterior crowding.
J Clin Pediatr Dent 30(1): 83-88, 2005