A patient with atypical Goldenhar
syndrome is reported. The characteristic features similar to the
other reported cases are facial asymmetry, multiple skin tags,
limbal dermoids and posteriorly angulated ear. The atypical intraoral
feature is unilateral presence of multiple complex odontomes.
The hypotrophy of left hemisphere with localized calcification
in the occipital and parietal regions of brain is also an additional
finding in this patient.
Key words: Goldenhar syndrome, oculoauriculovertebral spectrum,
dermoids, odontomes. |